{"id":98,"date":"2021-04-07T15:48:51","date_gmt":"2021-04-07T15:48:51","guid":{"rendered":"https:\/\/live-rawf.pantheonsite.io\/2021\/04\/07\/2021-4-7-hypothalamic-obesity-update-in-nords-rare-disease-database\/"},"modified":"2025-10-14T06:59:35","modified_gmt":"2025-10-14T06:59:35","slug":"2021-4-7-obesite-hypothalamique-mise-a-jour-dans-la-base-de-donnees-nords-sur-les-maladies-rares","status":"publish","type":"post","link":"https:\/\/www.rawoodfoundation.org\/fr\/2021\/04\/07\/2021-4-7-hypothalamic-obesity-update-in-nords-rare-disease-database\/","title":{"rendered":"Mise \u00e0 jour sur l'ob\u00e9sit\u00e9 hypothalamique dans la base de donn\u00e9es des maladies rares de NORD"},"content":{"rendered":"<div class=\"sqs-html-content\">\n<p class=\"\" style=\"white-space: pre-wrap;\">L'ob\u00e9sit\u00e9 hypothalamique (HO) est une maladie rare qui r\u00e9sulte souvent d'une l\u00e9sion de l'hypothalamus due \u00e0 une tumeur c\u00e9r\u00e9brale ou au traitement d'une tumeur c\u00e9r\u00e9brale. L'ob\u00e9sit\u00e9 hypothalamique peut entra\u00eener toute une s\u00e9rie de sympt\u00f4mes, dont l'hyperphagie, c'est-\u00e0-dire une augmentation anormale de l'app\u00e9tit d'intensit\u00e9 variable, et une prise de poids incontr\u00f4lable qui ne r\u00e9agit g\u00e9n\u00e9ralement pas au r\u00e9gime alimentaire ou \u00e0 l'exercice physique.<\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\">Il n'existe pas de v\u00e9ritable traitement fiable pour cette maladie, qui repr\u00e9sente un besoin substantiel non satisfait et dont les implications sont consid\u00e9rables. Non seulement il existe un risque d'ob\u00e9sit\u00e9 morbide, mais la faim incessante peut \u00eatre tr\u00e8s difficile \u00e0 supporter pour le patient, le personnel soignant et les membres de la famille. Les personnes qui souffrent \u00e0 long terme peuvent \u00eatre confront\u00e9es \u00e0 d'autres maladies chroniques, notamment le diab\u00e8te de type 2, la st\u00e9atose h\u00e9patique non alcoolique et les maladies cardiaques.<\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\">La communaut\u00e9 des patients souffrant d'ob\u00e9sit\u00e9 hypothalamique, les cliniciens traitants, les chercheurs et la Fondation Raymond A. Wood travaillent ensemble pour mieux communiquer la complexit\u00e9 de cette maladie et la diff\u00e9rencier de l'ob\u00e9sit\u00e9 classique, dans l'espoir de trouver des soins standard et de soutenir le d\u00e9veloppement d'un programme de recherche sur l'ob\u00e9sit\u00e9 hypothalamique. <a href=\"https:\/\/www.rawoodfoundation.org\/fr\/obesite-hypothalamique\/\" target=\"_blank\" rel=\"noopener\">traitement hypothalamique de l'ob\u00e9sit\u00e9<\/a> options.<\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\">Dans le cadre de cet effort, la d\u00e9finition de l'ob\u00e9sit\u00e9 hypothalamique a \u00e9t\u00e9 mise \u00e0 jour dans le document <a href=\"https:\/\/rarediseases.org\/\" target=\"_blank\" rel=\"noopener\">Organisation nationale pour les maladies rares<\/a> (NORD) pour refl\u00e9ter fid\u00e8lement le pronostic de l'HO, l'histoire, les signes et sympt\u00f4mes, les causes, le diagnostic, les th\u00e9rapies et les ressources.<\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\">RAWF remercie Shana E. McCormack, MD, MTR, directrice scientifique du centre neuroendocrinien de la division d'endocrinologie et de diab\u00e8te de l'h\u00f4pital pour enfants de Philadelphie ; M. Jennifer Abuzzahab, MD, endocrinologue p\u00e9diatrique au centre de diab\u00e8te p\u00e9diatrique McNeely et \u00e0 la clinique endocrinienne de l'h\u00f4pital pour enfants du Minnesota ; Ashley H. Shoemaker, MD, MSCI, professeur adjoint de p\u00e9diatrie, Vanderbilt University Medical Center ; et Christian L. Roth, MD, professeur, Seattle Children's Hospital, pour la pr\u00e9paration et la mise \u00e0 jour de ce rapport.<\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\"><a href=\"https:\/\/rarediseases.org\/rare-diseases\/hypothalamic-obesity-acquired\/\" target=\"_blank\" rel=\"noopener\">Lire le rapport complet ici \"<\/a><\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\"><a href=\"https:\/\/www.rawoodfoundation.org\/fr\/obesite-hypothalamique\/\">En savoir plus sur l'ob\u00e9sit\u00e9 hypothalamique \"<\/a><\/p>\n<p class=\"\" style=\"white-space: pre-wrap;\"><a href=\"https:\/\/www.rawoodfoundation.org\/fr\/faire-un-don\/\">Soutenez le travail de RAWF dans la recherche de solutions pour les survivants de tumeurs c\u00e9r\u00e9brales qui souffrent de cette maladie.<\/a><\/p>\n<\/div>\n<div class=\"image-block-outer-wrapper          layout-caption-below          design-layout-inline          combination-animation-none          individual-animation-none          individual-text-animation-none\" data-test=\"image-block-inline-outer-wrapper\"><\/p>\n<figure class=\"sqs-block-image-figure              intrinsic\" style=\"max-width: 1200px;\"><\/p>\n<div class=\"image-block-wrapper\" data-animation-role=\"image\">\n<div class=\"sqs-image-shape-container-element              has-aspect-ratio\" style=\"position: relative; padding-bottom: 66.66667175292969%; overflow: hidden; -webkit-mask-image: -webkit-radial-gradient(white, black);\"><\/p>\n<p><noscript><img decoding=\"async\" src=\"https:\/\/images.squarespace-cdn.com\/content\/v1\/587bc3d946c3c4be42a60e48\/1617810518552-WY5XGDYM8XDKPMHS2ARY\/ho-nord.jpg\" alt=\"ho-nord.jpg\" \/><\/noscript><img decoding=\"async\" class=\"thumb-image\" src=\"https:\/\/images.squarespace-cdn.com\/content\/v1\/587bc3d946c3c4be42a60e48\/1617810518552-WY5XGDYM8XDKPMHS2ARY\/ho-nord.jpg\" alt=\"ho-nord.jpg\" data-image=\"https:\/\/images.squarespace-cdn.com\/content\/v1\/587bc3d946c3c4be42a60e48\/1617810518552-WY5XGDYM8XDKPMHS2ARY\/ho-nord.jpg\" data-image-dimensions=\"1200x800\" data-image-focal-point=\"0.5,0.5\" data-load=\"false\" data-image-id=\"606dd456c94c3b395f8e70b4\" data-type=\"image\" \/><\/p>\n<\/div>\n<\/div>\n<\/figure>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>L'ob\u00e9sit\u00e9 hypothalamique (HO) est une maladie rare qui r\u00e9sulte souvent d'une l\u00e9sion de l'hypothalamus ... <a title=\"Mise \u00e0 jour sur l&#039;ob\u00e9sit\u00e9 hypothalamique dans la base de donn\u00e9es des maladies rares de NORD\" class=\"read-more\" href=\"https:\/\/www.rawoodfoundation.org\/fr\/2021\/04\/07\/2021-4-7-hypothalamic-obesity-update-in-nords-rare-disease-database\/\" aria-label=\"En savoir plus sur l&#039;ob\u00e9sit\u00e9 hypothalamique dans la base de donn\u00e9es des maladies rares de NORD\">Lire plus<\/a><\/p>","protected":false},"author":6,"featured_media":5594,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[29,1],"tags":[],"class_list":["post-98","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-hypothalamic-obesity","category-uncategorized","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-33","no-featured-image-padding"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Hypothalamic Obesity Update in NORD&#039;s Rare Disease Database - Raymond A. 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